Usher Syndrome is characterized by?

Usher Syndrome is characterized by?

• A. Stargardt's disease
• B. Glaucoma
• C. Usher Syndrome
• D. CHARGE syndrome

Answer: (C)

Usher syndrome is a genetic disorder that involves both hearing and vision. The defining feature is a dual sensory impairment: sensorineural hearing loss present from early life, combined with progressive vision loss caused by retinitis pigmentosa, a retinal degeneration that narrows the visual field and causes night blindness. Some individuals may also have vestibular (balance) problems, and intelligence is typically normal. This combination of hearing loss with retinal degeneration is what characterizes Usher syndrome.

Usher syndrome is a genetic disorder that involves both hearing and vision. The defining feature is a dual sensory impairment: sensorineural hearing loss present from early life, combined with progressive vision loss caused by retinitis pigmentosa, a retinal degeneration that narrows the visual field and causes night blindness. Some individuals may also have vestibular (balance) problems, and intelligence is typically normal. This combination of hearing loss with retinal degeneration is what characterizes Usher syndrome.